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Dernières publications
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Valentina Taglietti, Kaouthar Kefi, Lea Rivera, Oriane Bergiers, Nastasia Cardone, et al.. Thyroid-stimulating hormone receptor signaling restores skeletal muscle stem cell regeneration in rats with muscular dystrophy. Science Translational Medicine, 2023, 15 (685), ⟨10.1126/scitranslmed.add5275⟩. ⟨hal-04150315⟩
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A. Morin, Amalia Stantzou, Olga N. Petrova, John C.W. Hildyard, T. Tensorer, et al.. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle. Proceedings of the National Academy of Sciences of the United States of America, 2023, 120 (2), ⟨10.1073/pnas.2206324120⟩. ⟨hal-04122777⟩
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Chiffres clés
55
Publications avec texte intégral
Open Access
76 %
Mots clés
Diseases
Jonction neuromusculaire JNM
Dystrophie Musculaire de Becker BMD
Dystrophin central domain
Connexins
Calcium Channels
Human Umbilical Vein Endothelial Cells
Dilated Cardiomyopathy
CaVβs
Hepatocellular carcinoma
Becker muscular dystrophy
MiARN
Dystrophie Musculaire de Duchenne DMD
Multi exon skipping
Mitochondrial fission
Immunoglobulin Fc Fragments/pharmacology
Autophagy
Long noncoding RNA
Inbred mdx
Ex-vivo
Adult muscle stem cells
Isoformes
Cardiomyopathy
Isoforms
Cells
Becker BMD muscular dystrophy
Animals
Epigenetics
Inhibitors
Hear
Liver
Cachexia
Gene Expression Regulation/drug effects
Multi resolution modeling
Metabolism
Duchenne DMD dystrophy
L-Type
Dystrophine
Activin Receptors
Cell Biology
LKB1
Morphogenesis
Allele‐specific silencing therapy
Becker muscular dystrophy BMD
Base Sequence
Muscle Biology
Cell homeostasis
DHPR α1S
Knockout
LncARN
Molecular docking
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
Mdx mouse
Male
Drp1
LncRNA
Delivery
Dystrophin-EGFP
Genomic
Energy Metabolism/drug effects
CaVβ1
Modificateurs de gènes
Duchenne muscular dystrophy DMD
Becker Muscular Dystrophy
Skeletal muscle
Long QT
DMD
Heart Failure
Dynamin 2
Dystrophie myotonique de type 1 DM1
Animal/physiopathology
Antisense oligonucleotides
Duchenne muscular dystrophy
Humans
Calcium
Invivo
Génomique
Gene expression
Centronuclear myopathy
Gene modifiers
Cultured
Dystrophie musculaire de Becker
Cardiomyopathie
Multiresolution modeling
DMO
Dystrophin
Cell Line
CD38
Exon skipping
Clinical trials
Inbred C57BL
BMD
CaV subunits
Homeostasis
Mice
Dystrophy
Muscle
CTNNB1
MES
Molecular Sequence Data