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Myotonic Dystrophy type 1 Central nervous system DM1 Transgenic mouse model Oligodendrocyte ACETYLCHOLINESTERASE Animals RNA interference Dilated cardiomyopathy Exercise Brain dysfunction Heart failure Acetylcholinesterase deficiency Humans ARN BIOLOGIE MOLECULAIRE KNOCKOUT MICE Quantitative microdialysis Glucocorticoid-receptor Muscle Motoneuron Endurance training Transcriptomics Cells Myotonic Dystrophy Transgenic mouse Expression Aging Glucocorticoids Mouse model Myotonic dystrophy mouse models Hypoxia Glial cells Cultured Alternative splicing Neuron Trinucleotide repeat expansion Dystrophie Myotonique Cell model Maximal force Centronuclear myopathy Skeletal muscle CONGENITAL MYATHENIC SYNDROME RNA biology Fibrosis PacBio AAV Mouse models CRISPRi CMS Intermediate filament Cell culture model Desmin Duchenne muscular dystrophy Long read sequencing Thérapie génique MBNL Diaphragm Myotonic dystrophy Brain CTG repeat instability Antisense oligonucleotide PCR Therapy Oligodendrocytes Myotonic dystrophy type 1 DMPK Male Myostatin Dystrophin Cardiac muscle GSK3␤ Gene editing Myotonic Dystrophy Type 1 Autophagy Dynamin 2 DMSXL mice Acute coronary syndrome Acetylcholinesterase knockout mouse Dystrophie myotonique Antisense oligonucleotides CRISPR/Cas9 GABA Astrocytes Gene Therapy Trinucleotide Repeat Expansion Muscular dystrophy Glutamate Mice Cell penetrating peptide Cytoskeleton Astrocyte RNA splicing CTG repeat contractions Heart Gene therapy CTG repeats Genotype phenotype correlation Exercice Myelin